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Intermediate Maple Syrup Urine Disease
Known as:
MAPLE SYRUP URINE DISEASE, INTERMEDIATE
National Institutes of Health
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2 relations
Intermittent Maple Syrup Urine Disease
Broader (1)
Maple Syrup Urine Disease
Papers overview
Semantic Scholar uses AI to extract papers important to this topic.
2013
2013
Improved amino acid, bioenergetic metabolite and neurotransmitter profiles following human amnion epithelial cell transplant in intermediate maple syrup urine disease mice.
K. Skvorak
,
K. Dorko
,
+7 authors
S. Strom
Molecular Genetics and Metabolism
2013
Corpus ID: 33065583
2010
2010
Human Amnion Epithelial (hAE) Stem Cell Transplant Improves Disease Phenotype and Survival in the Intermediate Maple Syrup Urine Disease (iMSUD) Mouse Model
K. Skvorak
,
K. Dorko
,
+9 authors
S. Strom
2010
Corpus ID: 91022958
2009
2009
Hepatocyte Transplantation (HTx) Extends Lifespan, Increases Branched Chain a-Keto Acid Dehydrogenase (BCKDH) Activity,and Improves Neurotransmitter and Blood Amino Acid Profiles in a Murine Model of…
K. Skvorak
,
H. Paul
,
+10 authors
S. Strom
2009
Corpus ID: 90693955
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